Multifocal Rosai-Dorfman disease with involvement of the pinna
نویسندگان
چکیده
CRDD: cutaneous Rosai-Dorfman disease RDD: Rosai-Dorfman disease INTRODUCTION Rosai-Dorfman disease (RDD) is a benign nonLangerhans cell histiocytic disorder often involving the cervical lymph nodes. Extranodal disease was reported in 43% of patients with RDD in a review of the literature, with the skin reported to be the most common extranodal site. In the absence of lymph node involvement, RDD limited to the skin is termed cutaneous Rosai-Dorfman disease (CRDD). To date, only 5 cases of CRDD involving the ear have been reported. We present a case of multifocal CRDD with involvement of the right pinna.
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